Volume 14, Number 3, September 2002

Orthognathic Surgery in Achondroplasia: Case Report and Management Considerations

Somyot Lueveswanij, Thongchai Nuntanaranont
Department of Oral and Maxillofacial Surgery, Faculty of Dentistry, Prince of Songkhla University, Hat Yai, Songkla 90112, Thailand


Abstract
Achondroplasia is the most well known skeletal dysplasia and is characterised by disproportionate dwarfism. The typical facial skeletal dysmorphism includes an enlarged head with frontal and parietal bossing and prominence of the occiput. The midface is hypoplastic resulting in deficiency with a short nose and a depressed nasal bridge, upturned nostrils, and a flat zygomatic region. The mandible is relatively prognathic. Body step osteotomy of the mandible was used to correct the anterior open bite of a patient with achondroplasia, and the case is presented here. The perioperative management in terms of medical, anaesthetic, surgical, and specific maxillofacial considerations is discussed.

Key words:
Achondroplasia, Osteotomy

Asian J Oral Maxillofac Surg. 2002;14:161-167.
Comments
Respond to this article

Powered by JoomlaCommentCopyright (C) 2006 Frantisek Hliva. All rights reserved.Homepage: http://cavo.co.nr/